Wednesday, January 27, 2016

Isolated cardiac amyloidosis

Here is a case report and brief review. From the article:

Amyloidosis is a rare, multisystem disease characterized by deposition of fibrils in extracellular tissue that involves the kidney, liver, heart, autonomic nervous system, and several other organs.1 Based on the type of amyloid protein, cardiac involvement in amyloidosis can be seen in the following five types: (1) amyloid light chain (AL) or primary amyloidosis, (2) transthyretin (TTR) or familial/hereditary amyloidosis, (3) systemic senile amyloidosis, (4) isolated atrial amyloidosis, and (5) serum amyloid A (AA) or secondary amyloidosis.2 The diagnostic evaluation in suspected cardiac amyloidosis includes electrocardiography, echocardiography, and CMR and in certain cases requires a myocardial biopsy.

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